Ringed sideroblasts in βâ thalassemia
dc.contributor.author | Cattivelli, Kim | |
dc.contributor.author | Campagna, Dean R. | |
dc.contributor.author | Schmitz‐abe, Klaus | |
dc.contributor.author | Heeney, Matthew M. | |
dc.contributor.author | Yaish, Hassan M. | |
dc.contributor.author | Caruso Brown, Amy E. | |
dc.contributor.author | Kearney, Susan | |
dc.contributor.author | Walkovich, Kelly | |
dc.contributor.author | Markianos, Kyriacos | |
dc.contributor.author | Fleming, Mark D. | |
dc.contributor.author | Neufeld, Ellis J. | |
dc.date.accessioned | 2017-04-14T15:09:12Z | |
dc.date.available | 2018-07-09T17:42:24Z | en |
dc.date.issued | 2017-05 | |
dc.identifier.citation | Cattivelli, Kim; Campagna, Dean R.; Schmitz‐abe, Klaus ; Heeney, Matthew M.; Yaish, Hassan M.; Caruso Brown, Amy E.; Kearney, Susan; Walkovich, Kelly; Markianos, Kyriacos; Fleming, Mark D.; Neufeld, Ellis J. (2017). "Ringed sideroblasts in βâ thalassemia." Pediatric Blood & Cancer 64(5): n/a-n/a. | |
dc.identifier.issn | 1545-5009 | |
dc.identifier.issn | 1545-5017 | |
dc.identifier.uri | https://hdl.handle.net/2027.42/136352 | |
dc.description.abstract | Symptomatic βâ thalassemia is one of the globally most common inherited disorders. The initial clinical presentation is variable. Although common hematological analyses are typically sufficient to diagnose the disease, sometimes the diagnosis can be more challenging. We describe a series of patients with βâ thalassemia whose diagnosis was delayed, required bone marrow examination in one affected member of each family, and revealed ringed sideroblasts, highlighting the association of this morphological finding with these disorders. Thus, in the absence of characteristic congenital sideroblastic mutations or causes of acquired sideroblastic anemia, the presence of ringed sideroblasts should raise the suspicion of βâ thalassemia. | |
dc.publisher | Wiley Periodicals, Inc. | |
dc.subject.other | ringed sideroblasts | |
dc.subject.other | sideroblastic anemia | |
dc.subject.other | thalassemia | |
dc.title | Ringed sideroblasts in βâ thalassemia | |
dc.type | Article | en_US |
dc.rights.robots | IndexNoFollow | |
dc.subject.hlbsecondlevel | Pediatrics | |
dc.subject.hlbtoplevel | Health Sciences | |
dc.description.peerreviewed | Peer Reviewed | |
dc.description.bitstreamurl | https://deepblue.lib.umich.edu/bitstream/2027.42/136352/1/pbc26324.pdf | |
dc.description.bitstreamurl | https://deepblue.lib.umich.edu/bitstream/2027.42/136352/2/pbc26324_am.pdf | |
dc.identifier.doi | 10.1002/pbc.26324 | |
dc.identifier.source | Pediatric Blood & Cancer | |
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dc.owningcollname | Interdisciplinary and Peer-Reviewed |
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