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Deep cerebral vein expansion with metabolic and neurocognitive recovery in Sturgeâ Weber syndrome
dc.contributor.authorJohn, Flóra
dc.contributor.authorMaqbool, Mohsin
dc.contributor.authorJeong, Jeong‐won
dc.contributor.authorAgarwal, Rajkumar
dc.contributor.authorBehen, Michael E.
dc.contributor.authorJuhász, Csaba
dc.date.accessioned2018-05-15T20:15:45Z
dc.date.available2019-06-03T15:24:19Zen
dc.date.issued2018-04
dc.identifier.citationJohn, Flóra ; Maqbool, Mohsin; Jeong, Jeong‐won ; Agarwal, Rajkumar; Behen, Michael E.; Juhász, Csaba (2018). "Deep cerebral vein expansion with metabolic and neurocognitive recovery in Sturgeâ Weber syndrome." Annals of Clinical and Translational Neurology 5(4): 502-506.
dc.identifier.issn2328-9503
dc.identifier.issn2328-9503
dc.identifier.urihttps://hdl.handle.net/2027.42/143768
dc.description.abstractWe present longitudinal imaging data of a child with Sturgeâ Weber syndrome (SWS). At age 8 months, 3 weeks after initial seizures and prolonged motor deficit, MRI showed extensive right hemispheric SWS involvement with severe glucose hypometabolism on PET. She was treated with levetiracetam and aspirin. Followâ up imaging at age 29 months showed a robust interval expansion of enlarged deep medullary veins throughout the affected hemisphere along with a dramatic recovery of hemispheric metabolism and normalized neurocognitive functioning. These findings demonstrate a robust, multilobar hemispheric remodeling of deep venous collaterals that likely contributed to reversal of initial metabolic and neurocognitive deficits.
dc.publisherThe Sturgeâ Weber Foundation
dc.publisherWiley Periodicals, Inc.
dc.titleDeep cerebral vein expansion with metabolic and neurocognitive recovery in Sturgeâ Weber syndrome
dc.typeArticleen_US
dc.rights.robotsIndexNoFollow
dc.subject.hlbsecondlevelNeurology and Neurosciences
dc.subject.hlbtoplevelHealth Sciences
dc.description.peerreviewedPeer Reviewed
dc.description.bitstreamurlhttps://deepblue.lib.umich.edu/bitstream/2027.42/143768/1/acn3546_am.pdf
dc.description.bitstreamurlhttps://deepblue.lib.umich.edu/bitstream/2027.42/143768/2/acn3546.pdf
dc.identifier.doi10.1002/acn3.546
dc.identifier.sourceAnnals of Clinical and Translational Neurology
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dc.owningcollnameInterdisciplinary and Peer-Reviewed


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