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dc.contributor.authorMuenzer, Josephen_US
dc.contributor.authorBeekman III, Robert H.en_US
dc.contributor.authorProfera, Lisa M.en_US
dc.contributor.authorBove, Edward L.en_US
dc.date.accessioned2006-09-11T19:46:14Z
dc.date.available2006-09-11T19:46:14Z
dc.date.issued1993-03en_US
dc.identifier.citationMuenzer, Joseph; Beekman, Robert H.; Profera, Lisa M.; Bove, Edward L.; (1993). "Severe mitral insufficiency in mucopolysaccharidosis type III-B (Sanfilippo syndrome)." Pediatric Cardiology 14(2): 130-132. <http://hdl.handle.net/2027.42/48100>en_US
dc.identifier.issn0172-0643en_US
dc.identifier.issn1432-1971en_US
dc.identifier.urihttps://hdl.handle.net/2027.42/48100
dc.description.abstractA 6-year-old girl with mucopolysaccharidosis (MPS) III-B (Sanfilippo syndrome) who developed severe mitral regurgitation and congestive heart failure requiring surgery (valvuloplasty) is reported. One year after surgery the patient remains well, with marked improvement in her physical activity, and without signs of heart failure. This is only the second report of severe mitral regurgitation in MPS III, and is the first report of a successful repair (valvuloplasty) of a dysplastic mitral valve in the MPS. Mitral valvuloplasty should be considered instead of valve replacement in any MPS patient with mitral valve regurgitation requiring surgery.en_US
dc.format.extent688633 bytes
dc.format.extent3115 bytes
dc.format.mimetypeapplication/pdf
dc.format.mimetypetext/plain
dc.language.isoen_US
dc.publisherSpringer-Verlag; Springer-Verlag New York Inc.en_US
dc.subject.otherMitral Regurgitationen_US
dc.subject.otherValvuloplastyen_US
dc.subject.otherCardiologyen_US
dc.subject.otherMedicine & Public Healthen_US
dc.subject.otherMucopolysaccharidosesen_US
dc.subject.otherVascular Surgeryen_US
dc.subject.otherCardiac Surgeryen_US
dc.subject.otherSanfilippo Syndromeen_US
dc.subject.otherCongestive Heart Failureen_US
dc.titleSevere mitral insufficiency in mucopolysaccharidosis type III-B (Sanfilippo syndrome)en_US
dc.typeArticleen_US
dc.subject.hlbsecondlevelPublic Healthen_US
dc.subject.hlbsecondlevelPediatricsen_US
dc.subject.hlbtoplevelHealth Sciencesen_US
dc.description.peerreviewedPeer Revieweden_US
dc.contributor.affiliationumDivision of Biochemical Genetics and Metabolism, University of Michigan Medical School, Ann Arbor, Michigan, USA; Department of Pediatrics, MSRB II 3570B, University of Michigan Medical Center, Box 0688, 48109, Ann Arbor, MI, USAen_US
dc.contributor.affiliationumDivision of Cardiology, University of Michigan Medical School, Ann Arbor, Michigan, USAen_US
dc.contributor.affiliationumSection of Thoracic Surgery, Department of Surgery, University of Michigan Medical School, Ann Arbor, Michigan, USAen_US
dc.contributor.affiliationumDepartment of Pediatrics, MSRB II 3570B, University of Michigan Medical Center, Box 0688, 48109, Ann Arbor, MI, USAen_US
dc.contributor.affiliationumcampusAnn Arboren_US
dc.identifier.pmid8469632en_US
dc.description.bitstreamurlhttp://deepblue.lib.umich.edu/bitstream/2027.42/48100/1/246_2004_Article_BF00796996.pdfen_US
dc.identifier.doihttp://dx.doi.org/10.1007/BF00796996en_US
dc.identifier.sourcePediatric Cardiologyen_US
dc.owningcollnameInterdisciplinary and Peer-Reviewed


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