Esophageal involvement in epidermolysis bullosa dystrophica: Clinical and roentgenographic manifestations
dc.contributor.author | Ellis, Charles N. | en_US |
dc.contributor.author | Agha, Farooq P. | en_US |
dc.contributor.author | Francis, Isaac R. | en_US |
dc.date.accessioned | 2006-09-11T19:50:20Z | |
dc.date.available | 2006-09-11T19:50:20Z | |
dc.date.issued | 1983-12 | en_US |
dc.identifier.citation | Agha, Farooq P.; Francis, Isaac R.; Ellis, Charles N.; (1983). "Esophageal involvement in epidermolysis bullosa dystrophica: Clinical and roentgenographic manifestations." Gastrointestinal Radiology 8(1): 111-117. <http://hdl.handle.net/2027.42/48155> | en_US |
dc.identifier.issn | 0364-2356 | en_US |
dc.identifier.issn | 1432-0509 | en_US |
dc.identifier.uri | https://hdl.handle.net/2027.42/48155 | |
dc.identifier.uri | http://www.ncbi.nlm.nih.gov/sites/entrez?cmd=retrieve&db=pubmed&list_uids=6852425&dopt=citation | en_US |
dc.description.abstract | Epidermolysis bullosa is a rare hereditary mechanobullous skin disorder. Four patients with esophageal involvement are reported. These cases and review of reported cases of epidermolysis bullosa dystrophica-recessive (EBD-R) showed distinct clinical and roentgenographie features of esophageal involvement: diffuse inflammatory changes, motility disorders, small blisters or bullae seen as constant nodular-filling defects, esophageal ulcers, scars, pseudodiverticula, transverse and circumferential webs, various size strictures, shortening of the esophagus with development of traction hiatal hernia and gastroesophageal reflux, perforation, and complete obstruction of the esophageal lumen. Dysphagia is reversible when caused by bullae or webs and permanent when due to cicatrizing strictures. The strictures may remain unchanged in size for many years despite variations in dysphagic symptoms. | en_US |
dc.format.extent | 2312594 bytes | |
dc.format.extent | 3115 bytes | |
dc.format.mimetype | application/pdf | |
dc.format.mimetype | text/plain | |
dc.language.iso | en_US | |
dc.publisher | Springer-Verlag | en_US |
dc.subject.other | Gastroenterology | en_US |
dc.subject.other | Imaging / Radiology | en_US |
dc.subject.other | Medicine & Public Health | en_US |
dc.subject.other | Esophageal Stricture, Web, Ulcer, Perforation, Obstruction | en_US |
dc.subject.other | Esophagus, Inflammation | en_US |
dc.subject.other | Hepatology | en_US |
dc.subject.other | Epidermolysis Bullosa, Esophageal Involvement | en_US |
dc.title | Esophageal involvement in epidermolysis bullosa dystrophica: Clinical and roentgenographic manifestations | en_US |
dc.type | Article | en_US |
dc.subject.hlbsecondlevel | Radiology | en_US |
dc.subject.hlbsecondlevel | Internal Medicine and Specialties | en_US |
dc.subject.hlbtoplevel | Health Sciences | en_US |
dc.description.peerreviewed | Peer Reviewed | en_US |
dc.contributor.affiliationum | Department of Dermatology, University Hospital, University of Michigan Medical Center, Ann Arbor, Michigan, USA | en_US |
dc.contributor.affiliationum | Department of Radiology, University Hospital, University of Michigan Medical Center, Ann Arbor, Michigan, USA | en_US |
dc.contributor.affiliationum | Department of Radiology, University Hospital, University of Michigan Medical Center, Ann Arbor, Michigan, USA | en_US |
dc.contributor.affiliationumcampus | Ann Arbor | en_US |
dc.identifier.pmid | 6852425 | en_US |
dc.description.bitstreamurl | http://deepblue.lib.umich.edu/bitstream/2027.42/48155/1/261_2005_Article_BF01948101.pdf | en_US |
dc.identifier.doi | http://dx.doi.org/10.1007/BF01948101 | en_US |
dc.identifier.source | Gastrointestinal Radiology | en_US |
dc.owningcollname | Interdisciplinary and Peer-Reviewed |
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